Fat Embolism Syndrome in Duchenne Muscular Dystrophy Patients: Early Recognition and Aggressive Therapy
dc.contributor.author | Murphy, Lee D. | |
dc.contributor.author | Yabrodi, Mouhammad | |
dc.contributor.author | Lutfi, Riad | |
dc.contributor.department | Pediatrics, School of Medicine | en_US |
dc.date.accessioned | 2019-05-20T12:24:15Z | |
dc.date.available | 2019-05-20T12:24:15Z | |
dc.date.issued | 2018-06-04 | |
dc.description.abstract | We describe two pediatric patients with Duchenne muscular dystrophy that presented with acute neurologic deterioration and hypoxic respiratory failure requiring mechanical ventilation. These cases fulfill the clinical criteria for Fat Embolism Syndrome. Early recognition and aggressive supportive therapy with mechanical ventilation, right ventricular afterload reduction, and blood transfusion led to survival without any residual effects from the event. Fat Embolism Syndrome needs to be considered early in the course of patients with Duchenne muscular dystrophy who present with respiratory and neurological symptoms. | en_US |
dc.eprint.version | Final published version | en_US |
dc.identifier.citation | Murphy, L. D., Yabrodi, M., & Lutfi, R. (2018). Fat Embolism Syndrome in Duchenne Muscular Dystrophy Patients: Early Recognition and Aggressive Therapy. Case reports in critical care, 2018, 3686470. doi:10.1155/2018/3686470 | en_US |
dc.identifier.uri | https://hdl.handle.net/1805/19372 | |
dc.language.iso | en_US | en_US |
dc.publisher | Hindawi | en_US |
dc.relation.isversionof | 10.1155/2018/3686470 | en_US |
dc.relation.journal | Case Reports in Critical Care | en_US |
dc.rights | Attribution 3.0 United States | * |
dc.rights.uri | http://creativecommons.org/licenses/by/3.0/us/ | * |
dc.source | PMC | en_US |
dc.subject | Fat Embolism Syndrome | en_US |
dc.subject | Duchenne Muscular Dystrophy | en_US |
dc.subject | Aggressive Supportive Therapy | en_US |
dc.subject | Mechanical Ventilation | en_US |
dc.subject | Right Ventricular Afterload Reduction | en_US |
dc.subject | Blood Transfusion | en_US |
dc.subject | Respiratory Symptoms | en_US |
dc.subject | Neurological Symptoms | en_US |
dc.title | Fat Embolism Syndrome in Duchenne Muscular Dystrophy Patients: Early Recognition and Aggressive Therapy | en_US |
dc.type | Article | en_US |