Pirisinu, LauraDi Bari, Michele A.D’Agostino, ClaudiaMarcon, StefanoRiccardi, GeraldinaPoleggi, AnnaCohen, Mark L.Appleby, Brian S.Gambetti, PierluigiGhetti, BernardinoAgrimi, UmbertoNonno, Romolo2016-03-312016-03-312016Pirisinu, L., Bari, M. A. D., D’Agostino, C., Marcon, S., Riccardi, G., Poleggi, A., … Nonno, R. (2016). Gerstmann-Sträussler-Scheinker disease subtypes efficiently transmit in bank voles as genuine prion diseases. Scientific Reports, 6, 20443. http://doi.org/10.1038/srep204432045-2322https://hdl.handle.net/1805/9112Gerstmann-Sträussler-Scheinker disease (GSS) is an inherited neurodegenerative disorder associated with mutations in the prion protein gene and accumulation of misfolded PrP with protease-resistant fragments (PrPres) of 6–8 kDa.en-USAttribution 4.0 InternationalGerstmann-Sträussler-Scheinker diseaseneurodegenerative disorders6-8 kDaGerstmann-Sträussler-Scheinker disease subtypes efficiently transmit in bank voles as genuine prion diseases.Article