Charlagorla, PradeepkumarBreinholt, John P.2017-07-182017-07-182016-05Charlagorla, P., & Breinholt, J. P. (2016). Creating a Fontan fenestration in a child with dextrocardia and interrupted inferior vena cava. Annals of Pediatric Cardiology, 9(2), 179–182. http://doi.org/10.4103/0974-2069.173547https://hdl.handle.net/1805/13501Plastic bronchitis is a rare life-threatening complication of the Fontan operation. Transcatheter Fontan fenestration can ameliorate symptoms by decompressing elevated venous pressures. Transcatheter creation of a fenestration can be technically challenging in cases with complex venous anatomy. We report a case of a 5-year-old boy with heterotaxy, dextrocardia with unbalanced atrioventricular canal (AVC), atrial and visceral situs inversus, left-sided superior vena cava (SVC), and left-sided interrupted inferior vena cava (IVC) with azygos continuation. With few modifications to the equipment, a successful Fontan fenestration with stent implantation was performed via transjugular approach. At 2-year follow-up, his symptoms of plastic bronchitis improved significantly.en-USPublisher PolicyFenestrationHeterotaxyLateral tunnel fontanPlastic bronchitisTransjugular approachArticle