Kalra, VikasAkrawinthawong, KrittapoomKalra, MaitriJain, Rahul2023-05-082023-05-082022Kalra V, Akrawinthawong K, Kalra M, Jain R. Familial Hypertrophic Cardiomyopathy With Fasciculoventricular Accessory Pathway. JACC Case Rep. 2022;4(4):198-204. Published 2022 Feb 16. doi:10.1016/j.jaccas.2021.12.011https://hdl.handle.net/1805/32852Hypertrophic cardiomyopathy (HCM) is a common but an underdiagnosed condition. Fasciculoventricular bypass tract (FVBT) is rare. Concomitant presence of both conditions is well described in Danon disease. We report a case of familial HCM with FVBT linked to a heterozygous pathogenic variant, c.655G>C (p.Val219Leu), in the cardiac myosin binding protein C3 (MYBPC3) gene.en-USAttribution-NonCommercial-NoDerivatives 4.0 InternationalCardiac magnetic resonanceDanon diseaseElectrocardiogramFasciculoventricular bypass tractHypertrophic cardiomyopathyImplantable cardioverter-defibrillatorLysosome-associated membrane protein 2Cardiac myosin binding protein C3Nonsustained ventricular tachycardiaWolff-Parkinson-White syndromeAccessory pathwayHypertrophic cardiomyopathyFamilial Hypertrophic Cardiomyopathy With Fasciculoventricular Accessory PathwayArticle