Zhang, ShanxiangLong, Catherine2016-05-132016-05-132015-11Zhang, S., & Long, C. (2015). Pediatric Pharyngeal IgD-positive Monoclonal Plasmacytoid and Plasma Cell Neoplasm: Journal of Pediatric Hematology/Oncology, 37(8), 623–626. http://doi.org/10.1097/MPH.0000000000000330https://hdl.handle.net/1805/9583Pediatric neoplasm with monoclonal proliferation of lymphoplasmacytoid lymphocytes and plasma cells is exceedingly rare and has essentially never been reported in immunocompetent children. Here, we report a previously healthy 13-year-old girl with a pharyngeal mass and enlarged cervical lymph nodes. The pharyngeal mass was composed of CD138+, CD79a+, MUM-1+, IgD+, CD20−, PAX-5−, CD43−, λ-restricted monoclonal plasmacytoid, and plasma cells. Scattered CD20+, PAX-5+ B cells were present in the background. The patient was treated as localized non-Hodgkin lymphoma (stage II) with cyclophosphamide, doxorubicin, vincristine, and prednisone and is in complete remission at 17 months from the last chemotherapy.enPublisher Policyimmunocompetent childrenneoplasmlymphoplasmacytoid lymphocytesArticle